Case 2/2016 - Scimitar Sign with Right Pulmonary Vein Drainage into the Right Atrium
نویسندگان
چکیده
Clinical reasoning: the scimitar syndrome, due to the anomalous right pulmonary vein drainage, is clinically manifested as a simple atrial septal defect, with the described classic signs, few symptoms, ejection murmur in the pulmonary area, splitting of the second heart sound and right ventricular diastolic overload on the electrocardiogram. The scimitar sign on the chest X‐ray easily characterizes the diagnosis of the syndrome, as this diagnosis had been established in this case. Hence, the importance of this complementary radiographic assessment, simple and definitive, to achieve a diagnostic conclusion of this defect.
منابع مشابه
Syndrome of hypoplasia of the right lung and dextroposition of the heart: "scimitar sign" with normal pulmonary venous drainage.
Reported is a case in which the clinical findings of the scimitar syndrome were present but with termination of the anomalous pulmonary vein into the left atrium. There was hypoplasia of the right lung, dextroposition of the heart, and the scimitar sign in the right lower lung field. Cardiac catheterization revealed no shunt, and on pulmonary angiograms, a large common right pulmonary vein curv...
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